摘要:目的探讨Sturge-Weber综合征影像学表现及其诊断价值.方法回顾性分析6例Sturge-Weber综合征临床特征及其CT、MRI表现.结果6例均有单侧面部血管瘤及癫痫,1例血管瘤达头顶皮肤,3例CT可见患侧脑萎缩及钙化,2例同侧侧脑室扩大,1例双侧侧脑室扩大,1例患侧颅骨增厚,1例无异常发现;MRI所见脑萎缩及侧脑室扩大同CT所见,3例增强扫描显示病变范围明显大于CT和MRI平扫所见.结论通过CT和MRI影像学检查,特别以增强MRI扫描,对Sturge-Weber综合征的诊断有确诊价值.
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