摘要:患儿女,11岁.因颈后部发现肿块11年入院.查体:颈后部可见一约15×13cm大小的包块,质软,无压痛,边界清,表面散在数处皮肤呈青紫色,皮温无增高,听诊无血管杂音.神经系统检查未见异常.颈椎正位X线片可见一巨大软组织影,颈椎各椎体排列有序,C6、C7及T1、T2椎板裂(图1).CT示C6、C7椎体棘突不连,其后方为囊样低密度影,其内有分隔,约2.7×7cm大小,CT值为12~16Hu(图2、3).MRI示下颈椎脊膜、脊髓膨出,小脑扁桃体下疝(图4、5).诊断:(1)C6~C7脊膜、脊髓膨出.(2)Chiari畸形.
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