摘要:左心发育不良综合征(HLHS)是心脏左侧结构严重发育不全的复杂先天性心脏畸形,此类患儿自然预后差,病死率几乎达到100%.近年来主要通过分期矫治术和心脏移植使该病成为可治之症,术后存活的患者有相对正常的生活质量.
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